Ventricular arrhythmias in right ventricular dysplasia/cardiomyopathy

Hugh Calkins, Frank I. Marcus

Research output: Chapter in Book/Report/Conference proceedingChapter


Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a genetic cardiomyopathy characterized by ventricular arrhythmias and structural abnormalities of the right ventricle (RV). In ARVD/C there is progressive replacement of right ventricular myocardium with fatty and fibrous tissue. The precise prevalence of ARVD/C has been estimated to vary between 1 in 1000 and 1 in 5000 of the general population. The purpose of this chapter is to review the current understanding of ARVD/C and its management. Particular attention will be focused on some of the recent advances in the understanding of the genetic basis of ARVD/C and how this information provides insight into the mechanism of ventricular arrhythmias that can cause sudden death.

Original languageEnglish (US)
Title of host publicationElectrical Diseases of the Heart
Subtitle of host publicationGenetics, Mechanisms, Treatment, Prevention
PublisherSpringer London
Number of pages11
ISBN (Print)9781846288531
StatePublished - 2008

ASJC Scopus subject areas

  • General Medicine


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