The dementia of Gerstmann-Straussler-Scheinker Syndrome: Clinical variability demonstrated by two case reports

C. G. Lyketsos; M. Kraus

doi:10.1176/jnp.7.2.239

The dementia of Gerstmann-Straussler-Scheinker Syndrome: Clinical variability demonstrated by two case reports

C. G. Lyketsos, M. Kraus

School of Medicine

Research output: Contribution to journal › Article › peer-review

3 Scopus citations

Abstract

Two cases of Gerstmann-Straussler-Scheinker syndrome (GSS) are discussed in detail. These cases illustrate the variable clinical course and mostly cortical features of GSS-associated dementia. Given the availability of genetic tests that can now diagnose GSS, clinicians should consider these tests in cases where patients with dementia have extensive family histories or if the clinical course is atypical for Alzheimer's or vascular dementia.

Original language	English (US)
Pages (from-to)	239-242
Number of pages	4
Journal	Journal of Neuropsychiatry and Clinical Neurosciences
Volume	7
Issue number	2
DOIs	https://doi.org/10.1176/jnp.7.2.239
State	Published - Jan 1 1995

ASJC Scopus subject areas

Clinical Neurology
Psychiatry and Mental health

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abstract = "Two cases of Gerstmann-Straussler-Scheinker syndrome (GSS) are discussed in detail. These cases illustrate the variable clinical course and mostly cortical features of GSS-associated dementia. Given the availability of genetic tests that can now diagnose GSS, clinicians should consider these tests in cases where patients with dementia have extensive family histories or if the clinical course is atypical for Alzheimer's or vascular dementia.",

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AB - Two cases of Gerstmann-Straussler-Scheinker syndrome (GSS) are discussed in detail. These cases illustrate the variable clinical course and mostly cortical features of GSS-associated dementia. Given the availability of genetic tests that can now diagnose GSS, clinicians should consider these tests in cases where patients with dementia have extensive family histories or if the clinical course is atypical for Alzheimer's or vascular dementia.

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The dementia of Gerstmann-Straussler-Scheinker Syndrome: Clinical variability demonstrated by two case reports

Abstract

ASJC Scopus subject areas

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