Abstract
Children with skeletal dysplasia frequently have pulmonary disease which can be life threatening. These pulmonary problems are due to multiple aetiologies including thoracic and craniofacial anomalies predisposing to restrictive lung disease, upper airway obstruction and central apnoea. Recognition of pulmonary disease and early intervention improves the survival and quality of life for these children.
Original language | English (US) |
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Pages (from-to) | 365-371 |
Number of pages | 7 |
Journal | Paediatric Respiratory Reviews |
Volume | 2 |
Issue number | 4 |
DOIs | |
State | Published - 2001 |
Keywords
- Achondroplasia
- Central apnoea
- Cervicomedullary decompression
- Mucopolysaccharidoses
- Obstructive sleep apnoea syndrome
- Osteogenesis imperfecta
- Skeletal dysplasia
- Thoracic deformity
- Tonsillectomy and adenoidectomy
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Pulmonary and Respiratory Medicine