Simplified Mitral Valve Repair in Pediatric Patients With Connective Tissue Disorders

Luca A. Vricella, Duke E. Cameron, Narutoshi Hibino

Research output: Contribution to journalArticlepeer-review


Severe mitral valve regurgitation in children can stem from various congenital anomalies that involve the valvar and sub-valvar apparatus. In the rare subgroup of pediatric patients with connective tissue disorders, severe mitral regurgitation is typically associated with massive annular enlargement and severe bi-leaflet prolapse. We present our experience with a simplified form of repair that can result in mitral valve competency and low incidence of stenosis. This repair can be accomplished expeditiously in a group of patients who often present with compensated or decompensated heart failure or who might also need intervention on the aortic root.

Original languageEnglish (US)
Pages (from-to)121-128
Number of pages8
JournalOperative Techniques in Thoracic and Cardiovascular Surgery
Issue number3
StatePublished - Sep 1 2018


  • connective tissue disorders
  • loeys-dietz syndrome
  • marfan syndrome
  • mitral valve repair

ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine


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