Abstract
Introduction: Usually presenting in infancy, Leigh’s syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic. Case Presentation: We report a male patient with Leigh’s syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation. Conclusions: Dexmedetomidine with remifentanil can be used with no complication in this senerio.
Original language | English (US) |
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Article number | e28804 |
Journal | Anesthesiology and Pain Medicine |
Volume | 5 |
Issue number | 6 |
DOIs | |
State | Published - Dec 2015 |
Externally published | Yes |
Keywords
- Anesthesia
- Encephalomyelopathy
- Leigh’s syndrome
- Malignant hyperthermia
- Mitochondrial disorders
ASJC Scopus subject areas
- Anesthesiology and Pain Medicine