We report the MR findings in two patients with clinically and histologically proved Dejerine-Sottas disease. One patient had spinal involvement with multiple thickened and clumped nerve roots of the cauda equina; the second had multiple enlarged and enhancing cranial nerves. Although these findings are not specific for Dejerine-Sottas disease, they are suggestive of the diagnosis, which is further corroborated with history and confirmed with sural nerve biopsy and laboratory studies.
|Number of pages
|American Journal of Neuroradiology
|Published - Mar 1 1999
ASJC Scopus subject areas
- Radiology Nuclear Medicine and imaging
- Clinical Neurology