Abstract
The median predicted survival for people with cystic fibrosis (CF) is now over 45years of age, but despite tremendous advances in the management of CF, progressive respiratory failure remains the primary source of morbidity and mortality. CF is the third most common indication for lung transplantation in adults, after chronic obstructive pulmonary disease (COPD) and idiopathic pulmonary fibrosis (IPF), and the most common indication in the pediatric population. CF adults have the longest median survival of any group receiving lung transplants.
Original language | English (US) |
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Title of host publication | Encyclopedia of Respiratory Medicine, Second Edition |
Publisher | Elsevier |
Pages | 643-649 |
Number of pages | 7 |
Volume | 5 |
ISBN (Electronic) | 9780081027240 |
ISBN (Print) | 9780081027233 |
DOIs | |
State | Published - Jan 1 2021 |
Keywords
- Chronic obstructive pulmonary disease
- Cystic fibrosis related diabetes
- Extracorporeal life support
- Idiopathic pulmonary fibrosis
- Lung allocation score
ASJC Scopus subject areas
- General Medicine