Enlarging optic chiasmal glioma with stable visual acuity

A 13 1/2-year-old girl with stable, reduced visual acuity, nystagmus and small, pale optic discs initially noted at age 9 months, developed signs and symptoms of increased intracranial pressure. At craniotomy, an intrinsic glioma of the optic chiasm and both optic nerves extended into both frontal lobes, the hypothalamus and the third ventricle.