Desmoplastic small round cell tumor presenting as an inguinal mass in a 2-year old boy

Emma Kruger; Patience Obasaju; Emily Dunn; Jeffrey Lukish; Lindsay Goicochea; Christine A. Pratilas; Daniel S. Rhee

doi:10.1016/j.epsc.2020.101479

Desmoplastic small round cell tumor presenting as an inguinal mass in a 2-year old boy

Emma Kruger, Patience Obasaju, Emily Dunn, Jeffrey Lukish, Lindsay Goicochea, Christine A. Pratilas, Daniel S. Rhee

School of Medicine

Research output: Contribution to journal › Article › peer-review

Abstract

Desmoplastic small round cell tumor (DSRCT) is a highly aggressive soft tissue sarcoma that most commonly arises in the abdomen and pelvis and spreads over serosal surfaces, leading to abdominal pain or distention. Despite aggressive multimodal therapy, outcomes remain poor. It is most common in adolescents and young adults and reports in younger children are rare. We present a case of a 2-year-old male with the atypical presentation of a right groin mass, found to be DSRCT within an inguinal hernia.

Original language	English (US)
Article number	101479
Journal	Journal of Pediatric Surgery Case Reports
Volume	58
DOIs	https://doi.org/10.1016/j.epsc.2020.101479
State	Published - Jul 2020

Keywords

Desmoplastic small round cell tumor
Inguinal mass
Pediatric solid tumor

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Surgery

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10.1016/j.epsc.2020.101479

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title = "Desmoplastic small round cell tumor presenting as an inguinal mass in a 2-year old boy",

abstract = "Desmoplastic small round cell tumor (DSRCT) is a highly aggressive soft tissue sarcoma that most commonly arises in the abdomen and pelvis and spreads over serosal surfaces, leading to abdominal pain or distention. Despite aggressive multimodal therapy, outcomes remain poor. It is most common in adolescents and young adults and reports in younger children are rare. We present a case of a 2-year-old male with the atypical presentation of a right groin mass, found to be DSRCT within an inguinal hernia.",

keywords = "Desmoplastic small round cell tumor, Inguinal mass, Pediatric solid tumor",

author = "Emma Kruger and Patience Obasaju and Emily Dunn and Jeffrey Lukish and Lindsay Goicochea and Pratilas, {Christine A.} and Rhee, {Daniel S.}",

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AU - Kruger, Emma

AU - Obasaju, Patience

AU - Dunn, Emily

AU - Lukish, Jeffrey

AU - Goicochea, Lindsay

AU - Pratilas, Christine A.

AU - Rhee, Daniel S.

PY - 2020/7

Y1 - 2020/7

N2 - Desmoplastic small round cell tumor (DSRCT) is a highly aggressive soft tissue sarcoma that most commonly arises in the abdomen and pelvis and spreads over serosal surfaces, leading to abdominal pain or distention. Despite aggressive multimodal therapy, outcomes remain poor. It is most common in adolescents and young adults and reports in younger children are rare. We present a case of a 2-year-old male with the atypical presentation of a right groin mass, found to be DSRCT within an inguinal hernia.

AB - Desmoplastic small round cell tumor (DSRCT) is a highly aggressive soft tissue sarcoma that most commonly arises in the abdomen and pelvis and spreads over serosal surfaces, leading to abdominal pain or distention. Despite aggressive multimodal therapy, outcomes remain poor. It is most common in adolescents and young adults and reports in younger children are rare. We present a case of a 2-year-old male with the atypical presentation of a right groin mass, found to be DSRCT within an inguinal hernia.

KW - Desmoplastic small round cell tumor

KW - Inguinal mass

KW - Pediatric solid tumor

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ER -

Desmoplastic small round cell tumor presenting as an inguinal mass in a 2-year old boy

Abstract

Keywords

ASJC Scopus subject areas

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