Abstract
OBJECTIVE. Arterial dissection and aneurysm rupture are significant sources of morbidity and mortality in patients with connective tissue diseases. This article provides a detailed analysis of cardiovascular involvement in Marfan syndrome, Loeys-Dietz syndrome, and vascular Ehlers-Danlos syndrome. CONCLUSION. Although these syndromes share some overlapping features, they have discriminating clinical and imaging features, and knowledge of these features enables the radiologist to aid the referring clinician in making the correct diagnosis.
Original language | English (US) |
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Pages (from-to) | 1120-1129 |
Number of pages | 10 |
Journal | American Journal of Roentgenology |
Volume | 202 |
Issue number | 5 |
DOIs | |
State | Published - May 2014 |
Keywords
- Aneurysm
- CT angiography
- Ehlers-Danlos syndrome
- Loeys-Dietz syndrome
- Marfan syndrome
ASJC Scopus subject areas
- Radiology Nuclear Medicine and imaging