Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder

Rafael Ospino; Claire Brookmeyer

doi:10.1016/j.radcr.2023.10.078

Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder

Rafael Ospino, Claire Brookmeyer

School of Medicine

Research output: Contribution to journal › Article › peer-review

Abstract

Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm.

Original language	English (US)
Pages (from-to)	547-552
Number of pages	6
Journal	Radiology Case Reports
Volume	19
Issue number	2
DOIs	https://doi.org/10.1016/j.radcr.2023.10.078
State	Published - Feb 2024

Keywords

Computer tomography
Kaposiform lymphangiomatosis
Lymphatic anomalies
MTOR-inhibitors
Magnetic resonance

ASJC Scopus subject areas

Radiology Nuclear Medicine and imaging

Access to Document

10.1016/j.radcr.2023.10.078

Cite this

@article{7bcd1f55dd114ff38995bcf717fc5dd8,

title = "Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder",

abstract = "Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm.",

keywords = "Computer tomography, Kaposiform lymphangiomatosis, Lymphatic anomalies, MTOR-inhibitors, Magnetic resonance",

author = "Rafael Ospino and Claire Brookmeyer",

note = "Publisher Copyright: {\textcopyright} 2023",

year = "2024",

month = feb,

doi = "10.1016/j.radcr.2023.10.078",

language = "English (US)",

volume = "19",

pages = "547--552",

journal = "Radiology Case Reports",

issn = "1930-0433",

publisher = "Elsevier Inc.",

number = "2",

}

TY - JOUR

T1 - Challenging diagnosis of Kaposiform lymphangiomatosis

T2 - Unveiling a rare primary lymphatic disorder

AU - Ospino, Rafael

AU - Brookmeyer, Claire

PY - 2024/2

Y1 - 2024/2

N2 - Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm.

AB - Kaposiform lymphangiomatosis (KLA) is a rare and complex lymphatic anomaly associated with substantial morbidity and mortality. It features diffuse and multifocal malformed lymphatic channels, often leading to diagnostic difficulties due to its uncommon occurrence and non-specific clinical presentation. This case report emphasizes the crucial role of expert radiologists in accurately diagnosing a challenging KLA case initially mistaken for a neoplasm.

KW - Computer tomography

KW - Kaposiform lymphangiomatosis

KW - Lymphatic anomalies

KW - MTOR-inhibitors

KW - Magnetic resonance

UR - http://www.scopus.com/inward/record.url?scp=85177815867&partnerID=8YFLogxK

UR - http://www.scopus.com/inward/citedby.url?scp=85177815867&partnerID=8YFLogxK

U2 - 10.1016/j.radcr.2023.10.078

DO - 10.1016/j.radcr.2023.10.078

M3 - Article

C2 - 38074439

AN - SCOPUS:85177815867

SN - 1930-0433

VL - 19

SP - 547

EP - 552

JO - Radiology Case Reports

JF - Radiology Case Reports

IS - 2

ER -

Challenging diagnosis of Kaposiform lymphangiomatosis: Unveiling a rare primary lymphatic disorder

Abstract

Keywords

ASJC Scopus subject areas

Access to Document

Other files and links

Fingerprint

Cite this