Acute intrahepatic portal vein thrombosis complicating cholangitis in biliary atresia

C. Cuffari, E. Seidman, J. DuBois, P. Brochu, F. Alvarez

Research output: Contribution to journalArticlepeer-review

13 Scopus citations

Abstract

A 2-year-old boy with a Kasai portoenterostomy had systemic features suggestive of cholangitis and acute portal vein obstruction. The rapid rise in portal pressure caused a transient, severe decompensation of hepatic function. A superior mesenteric arterial angiogram confirmed the presence of diffuse intrahepatic portal vein thrombosis. Conclusion. This case provides clinical and radiological evidence supporting an association between ascending cholangitis and acute intrahepatic portal vein thrombosis.

Original languageEnglish (US)
Pages (from-to)186-189
Number of pages4
JournalEuropean Journal of Pediatrics
Volume156
Issue number3
DOIs
StatePublished - Mar 11 1997
Externally publishedYes

Keywords

  • Biliary atresia
  • Cholangitis
  • Intrahepatic portal vein thrombosis

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

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