Acute glaucoma in systemic mucopolysaccharidosis I-S

Harry A. Quigley, A. Edward Maumenee, Walter J. Stark

Research output: Contribution to journalArticlepeer-review

23 Scopus citations


Two siblings, a 56-year-old white man and a 44-year-old white woman, with systemic mucopolysaccharidosis I-S (Scheie's syndrome) developed acute glaucoma successively in each eye. Their management was complicated by an inability to visualize the anterior chamber angle due to corneal clouding by acid mucopolysaccharide (AMP) deposition. The mechanism of their glaucoma resembled angle closure, which may have been related to thickening of anterior ocular structures due to abnormal AMP storage.

Original languageEnglish (US)
Pages (from-to)70-72
Number of pages3
JournalAmerican journal of ophthalmology
Issue number1
StatePublished - Jul 1975

ASJC Scopus subject areas

  • Ophthalmology


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