A case report of lymphangioleiomyomatosis presenting as spontaneous pneumothorax

Ramon A. Riojas; Brady A. Bahr; David B. Thomas; John Perciballi; Lachland Noyes

doi:10.7205/MILMED-D-11-00333

A case report of lymphangioleiomyomatosis presenting as spontaneous pneumothorax

Ramon A. Riojas, Brady A. Bahr, David B. Thomas, John Perciballi, Lachland Noyes

Research output: Contribution to journal › Article › peer-review

Abstract

Spontaneous pneumothorax is a commonly encountered problem in the Emergency Department. Patients are often treated without further investigation for an underlying etiology. We present a patient who was unable to completely resolve a pneumothorax and was found to have lymphangioleiomyomatosis (LAM), a rare cystic lung disease. In the past, LAM was difficult to diagnose and had a mortality of 100% after 10 years, but now there is a 71% survival after 10 years. Recent research has led to increased characterization of the pathology and radiographic findings. This article briefly presents the case and discusses the etiology, diagnosis, and treatment of LAM.

Original language	English (US)
Pages (from-to)	477-480
Number of pages	4
Journal	Military medicine
Volume	177
Issue number	4
DOIs	https://doi.org/10.7205/MILMED-D-11-00333
State	Published - Apr 2012
Externally published	Yes

ASJC Scopus subject areas

Public Health, Environmental and Occupational Health

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abstract = "Spontaneous pneumothorax is a commonly encountered problem in the Emergency Department. Patients are often treated without further investigation for an underlying etiology. We present a patient who was unable to completely resolve a pneumothorax and was found to have lymphangioleiomyomatosis (LAM), a rare cystic lung disease. In the past, LAM was difficult to diagnose and had a mortality of 100% after 10 years, but now there is a 71% survival after 10 years. Recent research has led to increased characterization of the pathology and radiographic findings. This article briefly presents the case and discusses the etiology, diagnosis, and treatment of LAM.",

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AU - Noyes, Lachland

PY - 2012/4

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N2 - Spontaneous pneumothorax is a commonly encountered problem in the Emergency Department. Patients are often treated without further investigation for an underlying etiology. We present a patient who was unable to completely resolve a pneumothorax and was found to have lymphangioleiomyomatosis (LAM), a rare cystic lung disease. In the past, LAM was difficult to diagnose and had a mortality of 100% after 10 years, but now there is a 71% survival after 10 years. Recent research has led to increased characterization of the pathology and radiographic findings. This article briefly presents the case and discusses the etiology, diagnosis, and treatment of LAM.

AB - Spontaneous pneumothorax is a commonly encountered problem in the Emergency Department. Patients are often treated without further investigation for an underlying etiology. We present a patient who was unable to completely resolve a pneumothorax and was found to have lymphangioleiomyomatosis (LAM), a rare cystic lung disease. In the past, LAM was difficult to diagnose and had a mortality of 100% after 10 years, but now there is a 71% survival after 10 years. Recent research has led to increased characterization of the pathology and radiographic findings. This article briefly presents the case and discusses the etiology, diagnosis, and treatment of LAM.

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A case report of lymphangioleiomyomatosis presenting as spontaneous pneumothorax

Abstract

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